Infantile Lymphomatoid Granulomatosis in a Sudanese patient, description of a Case Report
Lymphomatoid granulomatosis (LYG) is a rare angiocentric and angiodestructive
Epstein-Barr virus-associated B-cell lymphoproliferative disorder (EBV-BLPD), varying widely from an indolent process to an aggressive large cell lymphoma, where the skin is considered as the extra pulmonary organ most commonly involved. We reported rare case, of a male infant, one year and 7 months old, presented with insidious onset of nasal bridge, easily bleed, scabbed, demarcated skin ulcer, with finger tip bullae, erosions and crusts. The case was diagnosed and confirmed histopathologically as Lymphomatoid granulomatosis, considered to be the first case of LYG been reported in Sudan.
Keywords: Lymphomatoid granulomatosis, Angiotropic lymphoma, Immunohistochemistry, Sudan.